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Prader-Willi Syndrome (USA) ALERT!!!

Risk of Stomach Necrosis and Rupture

Possibly Related to Chronic Gastroparesis

A Cause of Death from Sepsis, Gastric Necrosis or Blood Loss

Signs and symptoms of stomach necrosis and rupture:

  • Vomiting
    • Any vomiting is very unusual in Prader-Willi syndrome
  • Loss of appetite- (ominous sign)
  • Lethargy
  • Complaints of pain, usually non-specific
    • Pain sensation is abnormal in Prader-Willi syndrome due to high pain threshold; rarely complain of pain
    • Pain is often poorly localized
    • Peritoneal signs may be absent
  • Abdominal/stomach bloating and dilatation
  • Fever may or may not be present
    • Temperature regulation is altered in Prader-Willi syndrome
  • Guaiac positive stools (chronic gastritis)

THESE SIGNS SHOULD RAISE SUSPICION OF STOMACH NECROSIS/RUPTURE AS A POSSIBLE DIAGNOSIS WHICH CAN BE LIFE THREATENING!

History may include:

  • History of binge eating within the week
    • Hyperphagia and binge eating are characteristic of Prader-Willi syndrome, regardless of whether obese or slim
      • Frequently occurs after holiday, or social occasion with less supervision of intake
  • History of gastroparesis
    • Common in Prader-Willi syndrome, though often undiagnosed
  • Often slim or history of significant obesity followed by weight loss
    • May leave the stomach wall thinned


For more information call 800-926-4797.

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  Last edited 11/12/2010